B型食管闭锁的微妙表现
Subtle Presentation of Type B Esophageal Atresia.
Subtle Presentation of Type B Esophageal Atresia.
食管闭锁(EA)是一种罕见的前肠先天性畸形。目前已描述多种解剖变异,从单纯食管不连续到伴气管食管瘘的类型,其中某些变异的发生率远低于其他类型。一名早产儿(33周,1.5 kg)表现为腹部无气,鼻胃管在T4水平卷曲。支气管镜检查发现1级喉裂,无瘘管,符合A型食管闭锁,遂行胃造口术。初始6个椎体的缺损在六周内缩短至2.5个椎体。行Collis胃成形术及胸内吻合术。术后食管造影显示有一条通向气道的管道,提示B型食管闭锁。重复支气管镜检查证实了瘘管,经颈部入路予以关闭。恢复及随访影像学检查均无异常。B型食管闭锁罕见且容易被漏诊。重复影像学检查和支气管镜检查对于准确诊断和治疗至关重要。
Esophageal atresia (EA) is a rare congenital anomaly of the foregut. Several anatomic variants have been described, ranging from isolated esophageal discontinuity to forms associated with tracheoesophageal fistula, with some variants occurring far less frequently than others. A premature infant (33 weeks, 1.5 kg) presented with a gasless abdomen and a nasogastric tube coiled at T4. Bronchoscopy revealed a Grade 1 laryngeal cleft without fistula, consistent with type A EA, and a gastrostomy was placed. The initial six-vertebral gap shortened to 2.5 over six weeks. Collis gastroplasty and thoracic anastomosis were performed. Postoperative esophagram revealed a tract to the airway, suggesting a type B EA. Repeat bronchoscopy confirmed the fistula, which was closed via a cervical approach. Recovery and follow-up imaging were uneventful. Type B EA is rare and easily missed. Repeat imaging and bronchoscopy are crucial for accurate diagnosis and management.
Susana Fortich, Keyan Mobli, Esther Ewing, Ravi Radhakrishnan. Subtle Presentation of Type B Esophageal Atresia.. Cureus. 2026; doi:10.7759/cureus.107048.
Susana Fortich, Keyan Mobli, Esther Ewing, Ravi Radhakrishnan (2026). Subtle Presentation of Type B Esophageal Atresia.. Cureus. https://doi.org/10.7759/cureus.107048
Susana Fortich, Keyan Mobli, Esther Ewing, Ravi Radhakrishnan. Subtle Presentation of Type B Esophageal Atresia.[J]. Cureus, 2026 doi:10.7759/cureus.107048.
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